Opsoclonus myoclonus syndrome: response to plasmapheresis.
نویسندگان
چکیده
An 18-month-old with idiopathic opsomyoclonus, refractory to therapy with ACTH, corticosteroids, and clonazepam received plasmapheresis along with oral corticosteroids and azathioprine. The subject improved dramatically following this treatment. Anticerebellar antibodies were detected from the plasma in this patient and in a two and a half year-old girl with cerebellar ataxia secondary to an adrenal ganglioneuroma.
منابع مشابه
N-methyl-D-aspartate receptor autoimmune encephalitis presenting with opsoclonus-myoclonus: treatment response to plasmapheresis.
OBJECTIVES To report the clinical, laboratory, and radiographic features and the response to plasmapheresis in a patient with encephalopathy, opsoclonus, and myoclonus whose cerebrospinal fluid was positive for N-methyl-D-aspartate receptor-IgG. DESIGN Case report. SETTING St Marys Hospital, Rochester, Minnesota. PATIENT A 27-year-old woman with a history of episodic migraine developed su...
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عنوان ژورنال:
- Indian pediatrics
دوره 41 5 شماره
صفحات -
تاریخ انتشار 2004